Pulmonary Capillary Hemangiomatosis


Epidemiology


Physiology


Pathology


Diagnosis


Clinical

(the clinical presentations of [[Pulmonary Veno-Occlusive Disease]], pulmonary capillary hemangiomatosis, and [[Idiopathic Pulmonary Arterial Hypertension]] are often indistinguishable, prior to autopsy -> however, in contrast to [[Idiopathic Pulmonary Arterial Hypertension]], patients with [[Pulmonary Veno-Occlusive Disease]] and pulmonary capillary hemangiomatosis have crackles and clubbing on examination, ground glass opacities, septal thickening, mediastinal adenopathy on chest CT, hemosiderin-laden macrophages on BAL, lower DLCO, and more severe hypoxemia)


Treatment


Prognosis


References