Pulmonary Artery Angiosarcoma


In tumor obstruction, a tumor grows into the central pulmonary arteries, with additional appositional thrombosis leading to a progressive obstruction of proximal pulmonary arteries and PH. Such cases are due principally to pulmonary artery sarcomas, occur rarely, and are usually rapidly fatal (132,133). The differential diagnosis with CTEPH can be difficult. Computed tomography and magnetic resonance imaging angiography are the most useful diagnostic modalities for differentiation between tumor and thrombotic material (132,134,135).

Clinical Presentation