Immunoglobulin G4-Related Disease (IgG4-Related Disease)
Etiology
Clinical Manifestations
Pulmonary Manifestations
Bronchovascular Involvement
- Thickening of Bronchovascular Bundles and Interlobular Septa
Alveolar-Interstitial Involvement
- Honeycombing
- Bronchiectasis
- Diffuse Ground Glass Infiltrates
Round-Shaped, Ground Glass Infiltrates
Renal Manifestations
General Comments
- Epidemiology: most common renal manifestation
- May occur with membranous nephropathy
Membranous Nephropathy
- Epidemiology: less commonly observed than the acute interstitial nephritis
- However, may occur with acute interstitial nephritis
References